Prune Belly Syndrome: Length of Survival of a Patient with Renal Failure
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Abstract
Prune Belly syndrome is an uncommon congenital disorder characterized by altered abdominal musculature (hypoplasia), bilateral cryptorchidism and genitourinary tract abnormalities; this latter characteristic is determinant for the wide clinical variety that presents this disorder in the neonatal stage and, in addition, it is directly associated with the prognosis of the disease, since this depends on the degree of commitment of the renal function at the moment of the diagnosis . In this report, the case of a neonate with prenatal diagnosis
of this syndrome is presented, with multidisciplinary management during the neonatal period. An early and timely diagnostic-therapeutic approach is recommended to reduce the risk of complications and prolong survival in this type of patients.
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