Prune Belly sequence: a case report

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Willie Jack Blacio Vidal

Abstract

Background: The Prune-Belly sequence is a genetic disorder characterized by a triad that includes: weak abdominal wall musculature, urogenital anomalies, and bilateral cryptorchidism. Associated malformations usually accompany it. The surgical approach should be reserved for those patients with severe complications.
Clinical case: We present a male neonate with agenesis of the abdominal wall musculature, multicystic renal dysplasia, and bilateral cryptorchidism, which is transferred from a primary hospital in eastern Ecuador and attended in conservative management during his hospitalization.
Conclusions: The approach to SPB must be multidisciplinary due to its frequent association with other malformations. Prenatal diagnosis plays a fundamental role in the early detection of severe anomalies.

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How to Cite
Blacio Vidal, W. J. (2020). Prune Belly sequence: a case report. Pediatría, 53(1), 36–39. https://doi.org/10.14295/rp.v53i1.139
Section
Case report

References

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